presentamos un caso de displasia fibrosa monostótica localizada en el seno entre ellos el síndrome de albright (sólo en casos de displasia poliostótica). su. Displasia fibrosa monostótica e poliostótica. Front Cover. Simone Paula Bibliographic information. QR code for Displasia fibrosa monostótica e poliostótica. Download PDF. 1 / 3 Pages. Previous article. Go back to website. Next article.

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The recurrent behavior of Fibrous Dysplasia is essential to its surgical planning and it was also analyzed on this study. The unpolished glass appearance is due to polioshotica mixed mineralisation pattern of the lesion, that is, radiolucent areas corresponding to predominant fibrous tissue and more radiopaque areas corresponding to the bone tissue content 19 – Am J of Ophthal ; 3: Indications for surgical treatment include the following: Fibrous dysplasia is a benign fibrous-osseous lesion in which normal bone is replaced by fibrous connective tissue and immature bone, affecting only one monostotic or several bones polyostotic and mainly occurring in children and young adults.

However, in the majority of the cases, the unpolished glass appearance was the most prevalent image 8 Rua Casa do Ator, – cj. Other syndrome less common than polyostotic FD may be associated with Mazabraud syndrome, which is characterised by the involvement of soft tissues with presence of intra-muscular myxomas 511 – 1216 Ricalde P, Horswell BB. Fronto-orbital sphenoidal fibrous dysplasia.

Em geral afeta 1 em cada 4. Female patient aged 10 years old was referred to the radiology department for CBCT examination to investigate a painless hard oedema on the left side of the maxilla with unknown evolution and absence of painful symptoms. Br J OralMaxillofac Surg. Due to the unpolished glass appearance of FD on the images 13the imaging diagnosis is enough and thus bone biopsy is not necessary 8 This is due to the fact that the imaging aspects of FD are very distinctive.


Monostotic fibrous dysplasia: a case report with cone-beam computed tomography findings

Juiz de Fora, MG, Brasil. En bloc resection and bone graft: The polyostotic form is rarer and mainly occurring in long bones 610 and possibly associated with McCune-Albright syndrome, which is characterised by the presence of coffee-milk cutaneous pigmentation and endocrinopathy 136 – 1016 World J Surg Oncol.

Moreover, neurological symptoms such as headache, poor visual acuity, diplopia, paresthesia 1 – 2816 – 1720 – 21nasal obstruction 21621hearing loss 21720 and sinusitis-like symptoms 2 can occur when craniofacial bones are affected.

Services on Demand Journal. In some cases in which FD causes neither painful symptoms 7 nor aesthetical problems, there is no need of surgical treatment 1710which is recommended when maxilla and mandible are both affected by the lesion 1 Conservative treatment is usually based on treating asymptomatic cases of FD 6.

CT and MR imaging in a large series of patients with craniofacial fibrous dysplasia. One can also observe that the mucosa covering the affected bone appears to be healthy and normal 10 Rev Assoc Paul Cir Dent. Fibrous dysplasia is a pseudo-neoplastic lesion, ethiology unknown, benign and recurrent, which normal bone is replaced by fibrous tissue and lamelar bone trabeculae.

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Services on Demand Journal. Fibrous dysplasia in fibtosa maxilla: One can also observe an decreased maxillary sinus volume on the left side in the buccal-lingual sense, that is, located at the anterior region and extending towards the posterior region.

When present in these regions, FD can cause dental complications such as displacement of maxillary sinus floor and mandibular canal 2displacement or retention of teeth, loss of lamina dura, narrowing of the periodontal ligament space, and rarely, root resorption 21017 Although some studies reported the indication of magnetic resonance imaging MRI for diagnosis of FD 62026this type of examination does not reveal the distinctive characteristic of FD as observed in radiographs and CT images 6820since the lesion may often be confounded with tumours 68.


CBCT has provided important clinical contribution by allowing us to evaluate lesions in detail and the precise involvement of surrounding tissues, including pre-surgical evaluation when necessary and follow-up of the patients. Craniofacial and monostotic variants of fibrous dysplasia affecting themaxillofacial. We report a rare case of McCune Albright syndrome in a boy, who presented bilateral and diffuse involvement of orbits but few external craniofacial distortions.

This is an open-access article distributed under the terms of the Creative Commons Attribution License. O fibroma ossificante, apesar do crescimento lento, pode ter localmente comportamento mais agressivo. The diagnostic hypothesis was monostotic fibrous dysplasia. Services on Demand Journal.

Polioatotica of craniofacial fibrous dysplasia. One can observe slight prominence in the anterior and posterior regions of the left maxilla and partially-included tooth 21 with presence of orthodontic wire for traction.

The most common clinical symptom in the cases of craniofacial FD poliostotiica a painless swelling in the region involved, including facial asymmetry which may cause severe deformity resulting in functional and aesthetic compromise 6 It is worth emphasising that the initial lesions are more radiolucent, becoming more radiopaque as the lesion develops 16 The main differential diagnosis of the monostotic form on head and neck bones is Ossifying Fibroma which some consider another form of the same entity.

Alves 1Fernando Canavarros 2Daniela S. ABSTRACT Fibrous dysplasia is a benign fibrous-osseous lesion in which normal bone is replaced by fibrous connective tissue and immature bone, affecting only one monostotic or several bones polyostotic monostoyica mainly occurring in children and young adults. Artigo aceito em 20 de novembro de J Oral Maxillofac Surg.

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